Anesthetic management in a patient with SUSAC syndrome

a case report

Abstract

Susac’s Syndrome (SS) is defined as an occlusive microangiopathy of autoimmune etiology,
characterized by the involvement of arterioles in the cerebral, retinal, and cochlear vascular beds.
The classic clinical triad manifests as encephalopathy, visual deficits, and hearing loss. Given
its relative rarity and variable clinical presentation, SS frequently poses a diagnostic challenge,
resulting in underdiagnosis or misdiagnosis. Currently, the predominant therapy for SS involves
immunomodulation with corticotherapy. This case report describes the clinical course of a 36-yearold
female patient who underwent inhalational general anesthesia for elective laparoscopic
cholecystectomy. Although invasive intracranial pressure monitoring was not implemented, the
anesthetic management proved effective for the patient in question, highlighting the importance
of a detailed clinical and neurological evaluation in the perioperative period, even in procedures
considered to be of low neurological risk.